Le Clec'h G, Bourdinière J, Bourguet J, Faivre J, Le Marec B, Le Gall E
Ann Otolaryngol Chir Cervicofac. 1980 Jul-Aug;97(7-8):547-57.
Meningoencephalocoeles and nasal gliomas are congenital malformations rare in Europe but much better known in Morocco and in Thailand. These lesions have embryonic relations which are such that certain authors consider them to be only clinical varieties of the same malformation. They cause extra nasal, intra nasal or mixed tumours discovered most often at birth. Treatment is surgical either via a high intracranial approach or via a low facial approach (both approaches sometimes being used in association) and the prognosis is dominated by the problem of the dura mater if there are connections between the tumour mass and the subarachnoid spaces. When the problem is resolved by dural plasty, the later prognosis is excellent and, in particular, the psychomotor development of the children appears to be normal. Cosmetic problems, and in particular hypertelorism, may nevertheless require later surgery.
脑膜脑膨出和鼻胶质瘤是先天性畸形,在欧洲较为罕见,但在摩洛哥和泰国更为人所知。这些病变具有胚胎学关联,以至于某些作者认为它们只是同一畸形的临床变种。它们会导致鼻外、鼻内或混合型肿瘤,最常在出生时被发现。治疗方法是手术,可通过高颅内入路或低面部入路(有时两种入路联合使用),如果肿瘤块与蛛网膜下腔之间存在连接,预后则主要受硬脑膜问题的影响。当通过硬脑膜成形术解决该问题后,后期预后良好,尤其是儿童的精神运动发育似乎正常。然而,美容问题,特别是眼距过宽,可能仍需要后期手术。