由肠道细菌介导的戊二酸尿症。 - Suppr

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超能文献

Glutaric aciduria mediated by gut bacteria.

作者信息

Wendel U, Bakkeren J, de Jong J, Bongaerts G

机构信息

Department of Pediatrics, University Hospital of Nijmegen, The Netherlands.

出版信息

J Inherit Metab Dis. 1995;18(3):358-9. doi: 10.1007/BF00710431.

DOI:10.1007/BF00710431

PMID:7474906

Abstract

摘要

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Glutaric aciduria mediated by gut bacteria.由肠道细菌介导的戊二酸尿症。

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本文引用的文献

Glutaric, 3-hydroxypropionic, and lactic aciduria with metabolic acidemia, following extensive small bowel resection.

Biochem Med. 1982 Oct;28(2):229-36. doi: 10.1016/0006-2944(82)90074-6.

Implication of a peroxisomal enzyme in the catabolism of glutaryl-CoA.一种过氧化物酶体酶在戊二酰辅酶A分解代谢中的作用。

Biochem J. 1984 Jul 1;221(1):203-11. doi: 10.1042/bj2210203.

Glutaryl-coenzyme A dehydrogenase deficiency: a distinct encephalopathy.戊二酰辅酶A脱氢酶缺乏症：一种独特的脑病。

Pediatrics. 1991 Dec;88(6):1194-203.

Atypical riboflavin-responsive glutaric aciduria, and deficient peroxisomal glutaryl-CoA oxidase activity: a new peroxisomal disorder.非典型核黄素反应性戊二酸尿症及过氧化物酶体戊二酰辅酶A氧化酶活性缺乏：一种新的过氧化物酶体疾病。

J Inherit Metab Dis. 1991;14(2):165-73. doi: 10.1007/BF01800589.

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