Bartels C, Claeys L, Ktenidis K, Horsch S
Department of Vascular Surgery, Teaching Hospital, University of Cologne, Germany.
Angiology. 1995 Nov;46(11):1039-42. doi: 10.1177/000331979504601110.
Klippel-Trenaunay syndrome is characterized by the triad of unilateral port-wine hemangiomas, varicose veins, and hypertrophy of bone and soft tissue affecting one or more limbs. The rare F.P. Weber syndrome describes the mentioned entity and additional arteriovenous malformations. The association of an arterial aneurysm with the F.P. Weber syndrome has never been described in the current literature. A case of a brachial artery aneurysm in a patient with F.P. Weber syndrome is presented and the etiology of arterial aneurysm combined with congenital vascular abnormalities is discussed.
克-特综合征的特征为单侧葡萄酒色斑状血管瘤、静脉曲张以及影响一个或多个肢体的骨骼和软组织肥大三联征。罕见的F.P. 韦伯综合征描述了上述情况以及额外的动静脉畸形。目前文献中从未有过关于F.P. 韦伯综合征合并动脉瘤的报道。本文介绍了1例F.P. 韦伯综合征患者合并肱动脉瘤的病例,并探讨了合并先天性血管异常的动脉瘤的病因。