Stellbrink C, Kunze K P, Hanrath P
Medizinische Klinik I, RWTH Aachen, Germany.
Pacing Clin Electrophysiol. 1995 Sep;18(9 Pt 1):1717-20. doi: 10.1111/j.1540-8159.1995.tb06995.x.
A patient with hypertrophic cardiomyopathy (HCM) who presented with preexcitation pattern on the surface ECG suggestive of the Wolff-Parkinson-White (WPW) syndrome is described. Intracardiac electrophysiological study revealed a fixed anomalous QRS complex and a short-fixed His-ventricular interval indicating a fasciculoventricular Mahaim fiber. As this specific form of accessory connection does not cause reentrant tachycardias, no treatment was required. It is important to distinguish this entity from atriofascicular or nodoventricular Mahaim fibers or the WPW syndrome in patients with HCM showing a preexcitation pattern in the surface ECG, as these may cause life-threatening arrhythmias in this patient population.
本文描述了一名肥厚型心肌病（HCM）患者，其体表心电图呈现预激模式，提示存在 Wolff-Parkinson-White（WPW）综合征。心内电生理研究显示存在固定的异常 QRS 波群以及短固定的希氏束-心室间期，提示为束室型 Mahaim 纤维。由于这种特殊类型的附加连接不会引起折返性心动过速，因此无需治疗。对于体表心电图呈现预激模式的 HCM 患者，将此实体与房束型或结室型 Mahaim 纤维或 WPW 综合征相鉴别很重要，因为这些情况可能在该患者群体中导致危及生命的心律失常。
