Lacy D E, Spencer D A, Goldstein A, Weller P H, Darbyshire P
Children's Hospital, Middleway, Birmingham, U.K.
J Infect. 1993 Nov;27(3):301-4. doi: 10.1016/0163-4453(93)92271-w.
Two children who presented with fever, enlarged liver and spleen and ascites were found to have Pseudomonas cepacia septicaemia which proved fatal despite appropriate antibiotics and maximum supportive care. Chronic granulomatous disease of childhood (CGD) was subsequently diagnosed in both children. The possibility of CGD needs to be considered in any child with unexplained P. cepacia infection.
两名出现发热、肝脾肿大及腹水症状的儿童被发现患有洋葱伯克霍尔德菌败血症，尽管使用了适当的抗生素并给予了最大程度的支持治疗，但最终仍不治身亡。随后，这两名儿童均被诊断出患有儿童慢性肉芽肿病（CGD）。对于任何患有不明原因洋葱伯克霍尔德菌感染的儿童，都需要考虑患CGD的可能性。
