半侧巨脑伴室周异位——病例报告

Hemimegaloencephaly with periventricular heterotopia--case report.

作者信息

Sugiyama S, Fujii M, Nomura S, Yamashita T, Ito H, Hayashi T

机构信息

Department of Neurosurgery, Yamaguchi University School of Medicine.

出版信息

Neurol Med Chir (Tokyo). 1994 Aug;34(8):561-4. doi: 10.2176/nmc.34.561.

DOI:10.2176/nmc.34.561

PMID:7526246

Abstract

A 7-year-old girl was admitted with an unusual anomaly of hemimegaloencephaly associated with periventricular heterotopia manifesting as intractable seizures and mental retardation. Magnetic resonance (MR) imaging showed left hemispheric hypertrophy and left ventricular dilatation. Proton density-weighted MR imaging revealed a periventricular lesion isointense with gray matter. MR imaging is an effective method for diagnosing hemimegaloencephaly and heterotopia.

摘要

一名7岁女孩因半侧巨脑回畸形合并脑室周围异位的罕见异常情况入院，表现为难治性癫痫和智力发育迟缓。磁共振成像（MR）显示左侧大脑半球肥大和左心室扩张。质子密度加权磁共振成像显示脑室周围有一个与灰质等信号的病变。磁共振成像是诊断半侧巨脑回畸形和异位症的有效方法。