Yip A S, Chow W H, Lee D F, Cheung K L
Department of Cardiology, Grantham Hospital, University of Hong Kong, Aberdeen.
Clin Cardiol. 1995 Jul;18(7):424-5. doi: 10.1002/clc.4960180713.
A 33-year-old man was investigated for dyspnea on exertion and the presence of a pansystolic murmur. Physical examination revealed dextrocardia confirmed by chest radiograph, which also showed oligemic right lung field. Subsequent cardiac catheterization revealed secundum atrial septal defect, persistent left sided superior vena cava, and severe mitral valve prolapse causing severe mitral regurgitation with pulmonary hypertension. The right pulmonary artery was absent. It is the first report of the association between severe mitral valve prolapse and absent right pulmonary artery.
一名33岁男性因劳力性呼吸困难和全收缩期杂音接受检查。体格检查发现右位心，胸部X线片证实了这一点，该片还显示右肺野血供减少。随后的心导管检查显示继发孔型房间隔缺损、永存左上腔静脉以及严重二尖瓣脱垂导致严重二尖瓣反流伴肺动脉高压。右肺动脉缺如。这是关于严重二尖瓣脱垂与右肺动脉缺如相关性的首例报道。
