Pisoh T, Bhatia A, Oberlin C
Department of Orthopaedics and Traumatology, Hopital Bichat, Paris, France.
J Hand Surg Br. 1995 Jun;20(3):338-41. doi: 10.1016/s0266-7681(05)80090-7.
Vohwinkel syndrome or hereditary mutilating keratodermatitis is a rare condition producing palmoplantar hyperkeratosis and constricting rings of the fingers and toes which can progress to compromise neurovascular function and mobility. Medical treatment with oral retinol derivatives is recommended when its use is not contra-indicated. This paper describes surgical correction of the constricting rings on both hands in a 33-year-old woman affected by this condition.
沃温克尔综合征或遗传性致残性角皮病是一种罕见疾病，可导致掌跖角化过度以及手指和脚趾的缩窄环，病情进展可损害神经血管功能和活动能力。在无使用禁忌证时，建议采用口服视黄醇衍生物进行药物治疗。本文描述了一名33岁患此病女性双手缩窄环的手术矫正情况。
