I型酪氨酸血症：治疗策略的考量以及风险评估、饮食和移植方面的经验 - Suppr

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超能文献

Tyrosinaemia type I: considerations of treatment strategy and experiences with risk assessment, diet and transplantation.

作者信息

van Spronsen F J, Smit G P, Wijburg F A, Thomasse Y, Visser G, Heymans H S

机构信息

Beatrix Children's University Hospital, Groningen, The Netherlands.

出版信息

J Inherit Metab Dis. 1995;18(2):111-4. doi: 10.1007/BF00711742.

DOI:10.1007/BF00711742

PMID:7564222

Abstract

摘要

相似文献

Tyrosinaemia type I: considerations of treatment strategy and experiences with risk assessment, diet and transplantation.I型酪氨酸血症：治疗策略的考量以及风险评估、饮食和移植方面的经验

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Outcome of therapy of hereditary tyrosinemia.遗传性酪氨酸血症的治疗结果

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Plasma amino acid disturbance in infancy. I: Hypermethioninaemia and transient tyrosinaemia.婴儿期血浆氨基酸紊乱。I：高蛋氨酸血症和短暂性酪氨酸血症。

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本文引用的文献

Hereditary tyrosinemia type I: a new clinical classification with difference in prognosis on dietary treatment.遗传性I型酪氨酸血症：一种新的临床分类，饮食治疗的预后存在差异。

Hepatology. 1994 Nov;20(5):1187-91.

Liver transplantation in tyrosinaemia type I: the Groningen experience.

J Inherit Metab Dis. 1995;18(2):115-8. doi: 10.1007/BF00711743.

Pediatric liver transplantation.小儿肝移植

Transplant Proc. 1987 Aug;19(4):3230-5.

Tyrosinaemia type I: orthotopic liver transplantation as the only definitive answer to a metabolic as well as an oncological problem.I型酪氨酸血症：原位肝移植是解决代谢及肿瘤问题的唯一确切办法。

J Inherit Metab Dis. 1989;12 Suppl 2:339-42. doi: 10.1007/BF03335416.

Liver transplantation for hereditary tyrosinemia in the presence of hepatocellular carcinoma.存在肝细胞癌情况下的遗传性酪氨酸血症的肝移植

Transplant Proc. 1989 Feb;21(1 Pt 2):2445-6.

Hereditary tyrosinemia type I (chronic form): pathologic findings in the liver.遗传性I型酪氨酸血症（慢性型）：肝脏的病理表现

Hum Pathol. 1989 Feb;20(2):149-58. doi: 10.1016/0046-8177(89)90179-2.

The effects of early treatment of hereditary tyrosinemia type I in infancy by orthotopic liver transplantation.原位肝移植对婴儿期I型遗传性酪氨酸血症进行早期治疗的效果。

Transplantation. 1990 May;49(5):916-21. doi: 10.1097/00007890-199005000-00017.

Neurologic crises in hereditary tyrosinemia.遗传性酪氨酸血症中的神经危机

N Engl J Med. 1990 Feb 15;322(7):432-7. doi: 10.1056/NEJM199002153220704.

Liver transplantation for tyrosinemia. A review of 10 cases from the University of Pittsburgh.酪氨酸血症的肝移植。匹兹堡大学10例病例回顾。

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Early liver transplantation is indicated for tyrosinemia type I.对于Ⅰ型酪氨酸血症，建议早期进行肝移植。

J Pediatr Gastroenterol Nutr. 1991 Jul;13(1):10-5. doi: 10.1097/00005176-199107000-00002.

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