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[股四头肌肌病:一例迟发性局限性肌张力障碍类型]

[Quadriceps myopathy: a type of late focal dystrophy in a case].

作者信息

Cartier L, Hernández J E, Stuardo A, González J, Villagra R

机构信息

Departamento de Ciencias Neurológicas Oriente, Facultad de Medicina, Universidad de Chile, Santiago de Chile.

出版信息

Rev Med Chil. 1995 Jan;123(1):81-4.

PMID:7569450
Abstract

A 62 years old male with a slowly progressive focal myopathy is presented. He had noticed weakness in the lower limbs for three years and weakness in the upper limbs for one year. He had bilateral atrophy of quadriceps and biceps muscles, absence of knee jerks and hypertrophy of the calves. Needle EMG showed myopathic motor units. Hystological study was compatible with muscular dystrophy. The clinical and laboratory characteristics of this patient are in keeping with what has been described as "Quadriceps Myopathy" as a form of a muscular dystrophy.

摘要

本文报告了一名62岁男性,患有缓慢进展的局灶性肌病。他注意到下肢无力三年,上肢无力一年。他双侧股四头肌和肱二头肌萎缩,膝反射消失,小腿肥大。针电极肌电图显示肌病性运动单位。组织学研究符合肌肉营养不良。该患者的临床和实验室特征与被描述为“股四头肌肌病”的肌肉营养不良形式相符。

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