Scheid P, Anthoine D, Polu J M
Clinique Pneumologique Médico-Chirurgicale, CHU Brabois, Vandoeuvre-les-Nancy.
Rev Pneumol Clin. 1995;51(3):181-5.
Cystic fibrosis respiratory disease leads to chronic respiratory insufficiency, pulmonary hypertension and cor pulmonale. Clinical evaluation must be helped by diurnal artérial gasometry and nocturnal saturation measure, especially in acute phase and during the weeks after respiratory infections. Treatment of hypoxemia is based on oxygenotherapy, but also on nasal nocturnal ventilation for patients waiting for a pulmonary transplantation. Association of them is able to conserve or enhance respiratory and nutritional status.
囊性纤维化呼吸系统疾病会导致慢性呼吸功能不全、肺动脉高压和肺心病。临床评估必须借助日间动脉血气分析和夜间血氧饱和度测量，尤其是在急性期以及呼吸道感染后的几周内。低氧血症的治疗基于氧疗，但对于等待肺移植的患者也可采用夜间经鼻通气。两者联合能够维持或改善呼吸和营养状况。
