以多神经病为表现且生存期极长的原发性系统性淀粉样变性。

Primary systemic amyloidosis presenting with polyneuropathy characterized by very long survival.

作者信息

Rinaldi R, Azzimondi G, Preda P, Ricci P, D'Alessandro R, Pazzaglia P

机构信息

Neurology Unit, S. Orsola-Malpighi Hospital, Bologna, Italy.

出版信息

Acta Neurol Scand. 1995 Jun;91(6):511-3. doi: 10.1111/j.1600-0404.1995.tb00455.x.

DOI:10.1111/j.1600-0404.1995.tb00455.x

PMID:7572049

Abstract

We report a case of primary systemic amyloidosis associated with IgA monoclonal gammopathy presenting with sensorimotor polyneuropathy. For 10 years the neurological symptoms were the only clinical manifestation. A great deal of therapy was given right from the onset of symptoms and the very long survival of the patient may have been due to these efforts.

摘要

我们报告一例原发性系统性淀粉样变性病，与IgA单克隆丙种球蛋白病相关，表现为感觉运动性多神经病。10年来，神经症状是唯一的临床表现。从症状出现开始就给予了大量治疗，患者的长期存活可能归功于这些努力。