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伴有传导阻滞的缺血性神经病

[Ischemic neuropathy with conduction blocks].

作者信息

Traba A, Esteban A, Salinero E

机构信息

Sección de Neurofisiología Clínica, Hospital General Universitario Gregorio Marañón, Madrid.

出版信息

Neurologia. 1995 Aug-Sep;10(7):302-6.

PMID:7576730
Abstract

We present a patient with a clinical picture of multiple mononeuropathy in which muscle and sural nerve biopsy revealed the existence of vasculitis compatible with panarteritis nodosa. Along with classical axonal lesion signs, we observed multifocal conduction blocks (CB) in all the nerves explored electrophysiologically. Topographic evolution was atypical in that distal BC disappeared earlier, whereas proximal BC appeared later and in all cases persisted longer. Ischemia may play a pathogenic role in BC along with other more well-known factors such as compression and immunological processes. BC detection would probably be less exceptional if, when ischemic neuropathy is suspected, patients were subjected to early and follow-up electrophysiological exploration that included proximal nerve segments.

摘要

我们报告了一名患有多发性单神经病临床表现的患者,其肌肉和腓肠神经活检显示存在与结节性多动脉炎相符的血管炎。除了典型的轴索性病变体征外,我们在所有经电生理检查的神经中均观察到多灶性传导阻滞(CB)。其病变部位的演变不典型,表现为远端CB较早消失,而近端CB较晚出现且在所有病例中持续时间更长。缺血可能与其他更知名的因素如压迫和免疫过程一起在CB的发病机制中起作用。如果在怀疑缺血性神经病时,对患者进行包括近端神经节段的早期和随访电生理检查,CB的检出可能就不会那么罕见了。

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