Ortíz J, González San Martín F, Abad M, García Macías M C, Serrano E, Geijo F, Rodríguez A, Bullón A
Servicio de Anatomía Patológica, Hospital Clínico Universitario, Salamanca.
Rev Esp Enferm Dig. 1995 Aug;87(8):587-9.
We report a case of enteritis cystica profunda observed in a patient who, owing to both his personal and familial history, had been diagnosed and suffering from Peutz-Jeghers syndrome. The patient was operated because of a clinical picture of intestinal invagination. Together with hamartomatous polyps, anatomopathological study of the segment of the small intestine removed revealed the presence of lesions typical of Enteritis cystica profunda consisting in the presence of benign encysted glands and pools of mucous in the deep layers of the intestinal wall. The main characteristics of this interesting and rare entity are briefly commented.