Ciftci A O, Tanyel F C, Büyükpamukçu N, Hiçsönmez A
Department of Pediatric Surgery, Hacettepe University, Ankara, Turkey.
J Pediatr Surg. 1995 Apr;30(4):577-9. doi: 10.1016/0022-3468(95)90135-3.
Familial Mediterranean fever (FMF) is a disease characterized by recurring and self-limiting attacks of febrile serosal inflammation involving the peritoneal, synovial, and pleural membranes. Peritonitis is the most common clinical picture of FMF, and repeated acute abdominal episodes may result in formation of peritoneal adhesions that may cause adhesive small bowel obstruction (ASBO) requiring surgical intervention. This subject has neither been clarified nor thoroughly evaluated in the literature. The records of 355 pediatric patients diagnosed to have FMF were reviewed in order to clarify the incidence and outcome of ASBO without prior laparotomy during the course of FMF. The incidence rate has been found as 3% with no mortality. This figure shows ASBO to be the most frequent complication of FMF. Therefore this life-threatening surgical emergency should be kept in mind in the differential diagnosis of acute abdominal attacks during the course of FMF.
家族性地中海热(FMF)是一种以反复出现且自限性的发热性浆膜炎症发作为特征的疾病,累及腹膜、滑膜和胸膜。腹膜炎是FMF最常见的临床表现,反复的急性腹部发作可能导致腹膜粘连形成,进而可能引起粘连性小肠梗阻(ASBO),需要手术干预。该主题在文献中既未得到阐明,也未得到充分评估。回顾了355例诊断为FMF的儿科患者的记录,以明确FMF病程中未经事先剖腹手术的ASBO的发生率和结局。发现发生率为3%,无死亡病例。这一数字表明ASBO是FMF最常见的并发症。因此,在FMF病程中急性腹部发作的鉴别诊断中,应牢记这种危及生命的外科急症。