Schuijtvlot E T, Bax N M, Houwen R H, Hruda J
Department of Pediatric Surgery, University Children's Hospital Wilhelmina, Utrecht, The Netherlands.
J Pediatr Surg. 1995 Apr;30(4):589-90. doi: 10.1016/0022-3468(95)90138-8.
There appears to be a relationship between portal and pulmonary hypertension. A 5-year-old girl treated for biliary atresia developed this combination unexpectedly and died of pulmonary hypertension. Established pulmonary hypertension has a poor prognosis, which underscores the importance of early diagnosis by regular screening.