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Unexpected lethal pulmonary hypertension in a 5-year-old girl successfully treated for biliary atresia.

作者信息

Schuijtvlot E T, Bax N M, Houwen R H, Hruda J

机构信息

Department of Pediatric Surgery, University Children's Hospital Wilhelmina, Utrecht, The Netherlands.

出版信息

J Pediatr Surg. 1995 Apr;30(4):589-90. doi: 10.1016/0022-3468(95)90138-8.

DOI:10.1016/0022-3468(95)90138-8
PMID:7595841
Abstract

There appears to be a relationship between portal and pulmonary hypertension. A 5-year-old girl treated for biliary atresia developed this combination unexpectedly and died of pulmonary hypertension. Established pulmonary hypertension has a poor prognosis, which underscores the importance of early diagnosis by regular screening.

摘要

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