Lipsitz P J, Suser F, Weinberg S, Valderrama E
Am J Dis Child. 1979 Jan;133(1):76-8. doi: 10.1001/archpedi.1979.02130010082016.
Ichthyosiform erythroderma is a rare phenomenon occurring in about 1/300,000 live births. Congenital unilateral ichthyosis, described in this case report, is a clinical variant of ichthyosis. Only five previous cases have been reported. In the patient described in this report, superimposed infection of the affected skin developed. Her immunologic system was intact. She manifested failure to thrive, in spite of an adequate caloric intake, and markedly delayed psychomotor development. This patient also demonstrated absorption from the affected dermis of topically applied urea hydrophilic base ointment. She died before her first birthday.
鱼鳞癣样红皮病是一种罕见现象，约每30万例活产中出现1例。本病例报告中描述的先天性单侧鱼鳞病是鱼鳞病的一种临床变体。此前仅报告过5例。在本报告所述患者中，受累皮肤发生了叠加感染。她的免疫系统完好。尽管热量摄入充足，但她仍出现生长发育迟缓，且精神运动发育明显延迟。该患者还表现出从受累真皮吸收局部应用的尿素亲水性基质软膏的情况。她在1岁生日前去世。
