[Successful mitral valve plasty for mitral regurgitation combined with dilated cardiomyopathy in Noonan's syndrome].

We have experienced a mitral valve plasty for mitral regurgitation combined with dilated cardiomyopathy in a 21-year-old male patient with Noonan's syndrome, who had suffered from recurrent congestive heart failure. In echocardiography, severe mitral regurgitation and prolapse of the posterior mitral leaflet were noted. The left ventricle was dilated and the function was severely deteriorated. The plasty consisted of plication of the prolapsed posterior leaflet and annuloplasty with Carpentier ring. Intraoperative biopsy of the myocardium of the left ventricle showed an appearance consisting with dilated cardiomyopathy. Postoperatively the mitral regurgitation disappeared and the patient returned to his ordinary life.