Peiper M, Kalmár P, Kluth D, Lambrecht W
Abteilung für Kinderchirurgie, Chirurgische Universitätsklinik Hamburg.
Chirurg. 1995 Apr;66(4):445-7.
Bleeding of an aneurysm--especially of a great vessel--represents a complication of Ehlers-Danlos syndrome that is often lethal. A successful operation of a symptomatic aneurysm of the superior mesenteric artery in a 12-year old girl with an Ehlers-Danlos syndrome type VI is reported. The aneurysm was resected and replaced by a venous graft. Four years postoperatively the artery is perfectly patent; a new aneurysm did not develop.
动脉瘤出血——尤其是大血管的动脉瘤出血——是埃勒斯-当洛综合征的一种并发症，常常致命。本文报告了一例为一名患有Ⅵ型埃勒斯-当洛综合征的12岁女孩成功实施的肠系膜上动脉有症状动脉瘤手术。切除了动脉瘤，并用静脉移植物进行了置换。术后四年，动脉完全通畅；未出现新的动脉瘤。
