Nakano M, Tada K, Takahashi Y, Deguchi T, Kuriyama M, Ban Y, Kawada Y, Hanafusa J, Morita H, Yasuda K
Department of Urology, Gifu University School of Medicine.
Hinyokika Kiyo. 1995 Jul;41(7):529-32.
We treated a case of ACTH-independent bilateral adrenocortical macronodular hyperplasia (AIMAH), a rare disease. The patient was a 49 year-old man having chief complaints of facial edema, muscle wasting and typical Cushing's syndrome symptoms. He was diagnosed with AIMAH by specific hormonal tests for Cushing's syndrome and CT scan. Bilateral total adrenalectomy was performed in a two-stage operation for bilateral macronodular adrenocortical hyperplasia. The resected adrenal tumor weighed 57 g on the right side and 78 g on the left, and both had a yellowish nodular surface. The histological appearance was typical AIMAH. A total of 23 AIMAH reported cases was reviewed.
我们治疗了一例促肾上腺皮质激素非依赖性双侧肾上腺皮质大结节增生（AIMAH），这是一种罕见疾病。患者为一名49岁男性，主要症状为面部水肿、肌肉萎缩及典型的库欣综合征症状。通过针对库欣综合征的特定激素检测及CT扫描，他被诊断为AIMAH。针对双侧大结节性肾上腺皮质增生，分两阶段进行了双侧肾上腺全切术。切除的肾上腺肿瘤右侧重57克，左侧重78克，两者表面均呈黄色结节状。组织学表现为典型的AIMAH。我们回顾了总共23例已报道的AIMAH病例。
