Suzuki K, Tatsuno K, Mimori S, Murakami Y, Doi S, Takahashi Y, Kikuchi T, Mori K
Department of Pediatric Cardiology, Sakakibara Heart Institute, Tokyo, Japan.
Heart Vessels. 1995;10(3):158-62. doi: 10.1007/BF01744484.
Twins with pulmonary atresia, intact ventricular septum, and hypoplastic right ventricle associated with underdeveloped and discontinuous left pulmonary artery are described. Operations to connect the left pulmonary artery to the main pulmonary trunk, with subsequent biventricular repair assisted by bidirectional cavopulmonary anastomosis and atrial fenestration were performed. Follow-up catheterization proved spontaneous closure of the fenestration in one patient. Both patients have been in a satisfactory condition for 3 years since operation.
本文描述了患有肺动脉闭锁、室间隔完整、右心室发育不全且左肺动脉发育不良和中断的双胞胎病例。实施了将左肺动脉连接至主肺动脉的手术，随后在双向腔肺吻合术和心房开窗术辅助下进行双心室修复。随访导管检查证实其中一名患者的开窗自发闭合。自手术以来，两名患者均已保持3年的良好状态。
