Farre I, Copin M C, Boulanger E, Remy J, Wallaert B, Gosselin B
Service d'Anatomie et de Cytologie Pathologiques, Hôpital Calmette, CHU Lille.
Ann Pathol. 1995;15(1):59-62.
Erdheim-Chester disease is a rare visceral xanthogranulomatosis characterized by bilateral, symmetrical sclerosis of the metaphyseal regions of long bones and infiltration of foamy, lipid-laden histiocytes. Clinically, it ranges from an asymptomatic, focal process to a fatal, systemic disease. We report two new cases, different in their presentation and extension.
Erdheim-Chester病是一种罕见的内脏黄色肉芽肿病，其特征为长骨干骺端区域的双侧对称性硬化以及富含脂质的泡沫状组织细胞浸润。临床上，其表现范围从无症状的局灶性病变到致命的全身性疾病。我们报告两例新病例，其表现和累及范围有所不同。
