Pradhan S
Department of Neurology, Sanjay Gandhi Postgraduate Institute of Medical Science, Lucknow, India.
Pediatr Neurol. 1994 Nov;11(4):298-300. doi: 10.1016/0887-8994(94)90005-1.
A new sign in Duchenne muscular dystrophy is described. The sign demonstrates a unique characteristic of this disorder: selective hypertrophy and wasting in different muscles of the same region. The patients were asked to abduct their arms to about 90 degrees with elbows flexed to 90 degrees and hands directed upwards. Those who could not abduct the arm to 90 degrees were asked to do so to the maximum that they could. In this posture, all patients had examination of pectoral girdles from behind. Some patients with spinal muscular atrophy and other forms of muscular dystrophies were also examined in the same manner. In this posture, patients with Duchenne muscular dystrophy demonstrated a linear or oval depression (due to wasting) of the posterior axillary fold with hypertrophied or preserved muscles on its 2 borders (i.e., infraspinatus inferomedially and deltoid superolaterally), as if there were a valley between the 2 mounts. The sign was specific to Duchenne muscular dystrophy with sensitivity of about 90%. It was most remarkable in patients 8-11 years of age.
描述了杜氏肌营养不良症的一种新体征。该体征显示了这种疾病的一个独特特征：同一区域不同肌肉的选择性肥大和萎缩。要求患者将手臂外展至约90度，肘部弯曲至90度，手部向上。那些无法将手臂外展至90度的患者则被要求尽力做到最大程度。在此姿势下，从后方对所有患者的胸带进行检查。一些脊髓性肌萎缩症和其他形式肌营养不良症的患者也以同样的方式接受检查。在此姿势下，杜氏肌营养不良症患者的腋窝后皱襞呈现线性或椭圆形凹陷（由于萎缩），其两侧边界（即内侧下的冈下肌和外侧上的三角肌）肌肉肥大或保持正常，就好像两座山峰之间有一个山谷。该体征对杜氏肌营养不良症具有特异性，敏感性约为90%。在8至11岁的患者中最为明显。
