Baeza Herrera C, Velasco Soria L, Domínguez Pérez S T, Baeza Herrera M S
Departamento de Cirugía, Hospital Pediátrico Moctezuma, México, D.F.
Rev Gastroenterol Mex. 1994 Oct-Dec;59(4):304-7.
Peutz-Jeghers syndrome is a autosomal dominant disorder characterized by hamartomatous polyposis of the gastrointestinal tract and mucocutaneous melanin pigmentation. This condition can occur and cause symptoms at any age, but intestinal obstruction due to intussusception is a frequent complication. Two cases of this syndrome associated to intussusception are reported. Both patients were girls, 2 and 8 years old respectively and underwent surgical treatment.
佩-吉二氏综合征是一种常染色体显性疾病,其特征为胃肠道错构瘤性息肉病和皮肤黏膜黑色素沉着。这种病症可在任何年龄出现并引发症状,但肠套叠所致肠梗阻是常见并发症。本文报告两例与肠套叠相关的该综合征病例。两名患者均为女孩,分别为2岁和8岁,均接受了手术治疗。