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Etiology and pathogenesis of prion diseases.

作者信息

DeArmond S J, Prusiner S B

机构信息

Department of Pathology, University of California, San Francisco, USA.

出版信息

Am J Pathol. 1995 Apr;146(4):785-811.

PMID:7717447
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1869256/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/c9e222c68063/amjpathol00052-0022-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/bd6b3a16f4f5/amjpathol00052-0011-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/e2691c4bc35f/amjpathol00052-0012-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/717103c35740/amjpathol00052-0016-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/10888f2ba7e1/amjpathol00052-0018-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/7b47af41fcbf/amjpathol00052-0019-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/f1b3d9735173/amjpathol00052-0020-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/a6078393b146/amjpathol00052-0021-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/c9e222c68063/amjpathol00052-0022-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/bd6b3a16f4f5/amjpathol00052-0011-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/e2691c4bc35f/amjpathol00052-0012-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/717103c35740/amjpathol00052-0016-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/10888f2ba7e1/amjpathol00052-0018-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/7b47af41fcbf/amjpathol00052-0019-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/f1b3d9735173/amjpathol00052-0020-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/a6078393b146/amjpathol00052-0021-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/146d/1869256/c9e222c68063/amjpathol00052-0022-a.jpg

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本文引用的文献

1
[The hereditary form of Creutzfeldt-Jakob disease (the Backer family)].[克雅氏病的遗传形式（巴克尔家族）]
Arch Psychiatr Nervenkr Z Gesamte Neurol Psychiatr. 1950;184(7):653-74. doi: 10.1007/BF00344941.
2
DEGENERATION OF THE CEREBELLAR AND HYPOTHALAMONEUROHYPOPHYSIAL SYSTEMS IN SHEEP WITH SCRAPIE; AND ITS RELATIONSHIP TO HUMAN SYSTEM DEGENERATIONS.患瘙痒病绵羊的小脑和下丘脑神经垂体系统的退化；及其与人类系统退化的关系。
Brain. 1964 Mar;87:153-76. doi: 10.1093/brain/87.1.153.
3
NEURONAL ENZYMATIC FAILURE IN CREUTZFELDT-JAKOB DISEASE; A FAMILIAL STUDY.
4
The Effect of Valeton (Zingiberaceae) Extract on Prion Propagation in Cell-Based and Animal Models.姜黄提取物对基于细胞和动物模型的朊病毒传播的影响。
Int J Mol Sci. 2022 Dec 22;24(1):182. doi: 10.3390/ijms24010182.
5
Minimal change prion retinopathy: Morphometric comparison of retinal and brain prion deposits in Creutzfeldt-Jakob disease.微小病变朊病毒视网膜病变：克雅氏病中视网膜和脑部朊病毒沉积的形态计量学比较。
Exp Eye Res. 2022 Sep;222:109172. doi: 10.1016/j.exer.2022.109172. Epub 2022 Jul 6.
6
Prion Pathogenesis Revealed in a Series of the Special Issues "Prions and Prion Diseases".朊病毒发病机制在一系列特刊“朊病毒和朊病毒疾病”中得到揭示。
Int J Mol Sci. 2022 Jun 10;23(12):6490. doi: 10.3390/ijms23126490.
7
The first non-prion pathogen identified: neurotropic influenza virus.首例非朊病毒病原体被发现：神经亲和性流感病毒。
Prion. 2022 Dec;16(1):1-6. doi: 10.1080/19336896.2021.2015224.
8
Virus Infection, Genetic Mutations, and Prion Infection in Prion Protein Conversion.病毒感染、遗传突变和朊病毒感染在朊病毒蛋白转化中的作用。
Int J Mol Sci. 2021 Nov 18;22(22):12439. doi: 10.3390/ijms222212439.
9
Ethanolamine Is a New Anti-Prion Compound.乙醇胺是一种新型抗朊病毒化合物。
Int J Mol Sci. 2021 Oct 29;22(21):11742. doi: 10.3390/ijms222111742.
10
Human cerebral organoids as a therapeutic drug screening model for Creutzfeldt-Jakob disease.人类大脑类器官作为克雅氏病的治疗药物筛选模型。
Sci Rep. 2021 Mar 9;11(1):5165. doi: 10.1038/s41598-021-84689-6.
Arch Neurol. 1964 Feb;10:181-95. doi: 10.1001/archneur.1964.00460140067009.
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Kuru; clinical, pathological and epidemiological study of an acute progressive degenerative disease of the central nervous system among natives of the Eastern Highlands of New Guinea.库鲁病；新几内亚东部高地原住民中一种中枢神经系统急性进行性退行性疾病的临床、病理及流行病学研究
Am J Med. 1959 Mar;26(3):442-69. doi: 10.1016/0002-9343(59)90251-7.
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The skeletal muscle of sheep affected with scrapie.
J Comp Pathol. 1958 Apr;68(2):264-74. doi: 10.1016/s0368-1742(58)80027-2.
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Degenerative disease of the central nervous system in New Guinea; the endemic occurrence of kuru in the native population.新几内亚的中枢神经系统退行性疾病；当地人群中库鲁病的地方性流行。
N Engl J Med. 1957 Nov 14;257(20):974-8. doi: 10.1056/NEJM195711142572005.
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Myopathy in sheep; its relationship to scrapie and to dermatomyositis and muscular dystrophy.绵羊的肌病；其与羊瘙痒病、皮肌炎及肌肉萎缩症的关系。
Lancet. 1956 Oct 13;271(6946):737-46. doi: 10.1016/s0140-6736(56)90957-6.
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Novel missense variants of prion protein in Creutzfeldt-Jakob disease or Gerstmann-Sträussler syndrome.克雅氏病或格斯特曼-施特劳斯勒综合征中朊病毒蛋白的新型错义变体。
Biochem Biophys Res Commun. 1993 Mar 15;191(2):709-14. doi: 10.1006/bbrc.1993.1275.
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Structural studies of the scrapie prion protein using mass spectrometry and amino acid sequencing.利用质谱法和氨基酸测序对瘙痒病朊病毒蛋白进行结构研究。
Biochemistry. 1993 Mar 2;32(8):1991-2002. doi: 10.1021/bi00059a016.
10
Creutzfeldt-Jakob disease in a physician: a review of the disorder in health care workers.
Neurology. 1993 Jan;43(1):205-6. doi: 10.1212/wnl.43.1_part_1.205.