Szopiński J, Kamiński Z, Bestry I, Bogdan J
III Kliniki Gruźlicy i Chorób Płuc.
Pneumonol Alergol Pol. 1994;62(11-12):634-9.
Pulmonary arteriovenous fistulas are rare congenital malformations associated in 40% of cases with Osler-Weber-Rendu disease. PAF acquired in connection with the chest trauma, surgery and some inflammatory or neoplastic lung diseases were also described. In the Institute of Tuberculosis and Chest Diseases we have observed 11 cases of congenital PAF in 4000 resected lungs during the last years. In this report we described one more case with PAF. A 40 years old man was admitted to the Institute of Tuberculosis and Chest Diseases with hemoptysis. History and physical examination was unremarkable. Chest roentgenogram revealed a right upper lobe infiltrate. Tuberculosis or cancer was suspected and during the diagnostic procedures antituberculous drugs were given. After 3 weeks of treatment hemoptysis increased and chest roentgenogram revealed progression of the infiltrate in the right upper lobe and new lesions in the middle lobe. According to the character of X-ray progression which night be characteristic of active bleeding, a possibility of arteriovenous fistulas could not be excluded. As life threatening haemorrhage persisted right upper lobectomy without angiography was done. In the resected lobe arteriovenous fistulas were found. Angiography after operation was proposed but was refused by the patient. He is now well and symptoms free 5 months.
肺动静脉瘘是一种罕见的先天性畸形,40%的病例与遗传性出血性毛细血管扩张症相关。也有关于因胸部创伤、手术以及一些肺部炎性或肿瘤性疾病而获得性肺动静脉瘘的描述。在过去几年中,结核病与胸部疾病研究所于4000例肺切除病例中观察到11例先天性肺动静脉瘘。在本报告中,我们又描述了1例肺动静脉瘘病例。一名40岁男性因咯血入住结核病与胸部疾病研究所。病史和体格检查均无异常。胸部X线片显示右上叶有浸润影。怀疑为肺结核或癌症,在诊断过程中给予了抗结核药物治疗。治疗3周后咯血加重,胸部X线片显示右上叶浸润影进展,中叶出现新病灶。根据可能为活动性出血特征的X线进展特点,不能排除动静脉瘘的可能性。由于威胁生命的出血持续存在,在未进行血管造影的情况下实施了右上叶切除术。在切除的肺叶中发现了动静脉瘘。术后建议进行血管造影,但患者拒绝。他现在情况良好,5个月来无症状。