Spellman J E, Driscoll D L, Huben R P
Department of Surgical Oncology, Roswell Park Cancer Institute, Buffalo, New York 14263, USA.
Am Surg. 1995 May;61(5):456-9.
Primary renal sarcoma represents approximately 1 per cent of all primary tumors of the kidney. The purpose of this study is to review the experience at Roswell Park Cancer Institute with the treatment of primary renal sarcoma. Four patients with a diagnosis of primary renal sarcoma admitted from 1976 to 1983 form the basis of this review. All patients underwent radical nephrectomy. The tumor was localized in two patients, and locally invasive in two patients. All patients had recurrence of metastatic disease. Patients with localized disease recurred at 19.0 and 25.0 months respectively. Patients with invasive disease recurred at 4.0 and 5.0 months respectively. Patients presenting with localized disease survived a mean of 34.0 months. Patients presenting with invasive disease died at 6.0 and 10.0 months from time of diagnosis. Primary renal sarcoma is a rare entity. Only patients presenting with localized disease have a reasonable chance for prolonged survival.
原发性肾肉瘤约占所有原发性肾肿瘤的1%。本研究的目的是回顾罗斯威尔公园癌症研究所治疗原发性肾肉瘤的经验。1976年至1983年收治的4例原发性肾肉瘤患者构成了本综述的基础。所有患者均接受了根治性肾切除术。2例患者肿瘤局限，2例患者肿瘤局部浸润。所有患者均出现转移性疾病复发。局限性疾病患者分别在19.0个月和25.0个月复发。浸润性疾病患者分别在4.0个月和5.0个月复发。表现为局限性疾病的患者平均存活34.0个月。表现为浸润性疾病的患者在诊断后6.0个月和10.0个月死亡。原发性肾肉瘤是一种罕见的疾病。只有表现为局限性疾病的患者才有合理的机会获得长期生存。
