Shepherd P, Suffolk R, Halsey J, Allan N
Department of Medicine, Western General Hospital, Edinburgh.
Br J Haematol. 1995 Mar;89(3):546-54. doi: 10.1111/j.1365-2141.1995.tb08362.x.
Two hundred and nineteen cases of Ph+ve CML and 15 Ph-ve, BCR+ve CML cases have been analysed to determine the breakpoint site and its relationship to clinical features, cytogenetic response, duration of chronic phase and survival. 119 cases have had RNA analysis performed to determine the type of BCR/ABL transcript and have also been analysed in a similar way. Presenting features at diagnosis including age, sex, white-cell count and platelet count showed no significant difference for those with 5' and 3' breakpoints and those with either b2a2 or b3a2 BCR/ABL transcripts. However, in a subgroup of patients whose presenting white-cell count was < 100 x 10(9)/l, those with b3a2 transcript did have a significantly higher platelet count. Analysis by Sokal risk grouping showed no difference for 5' or 3' breakpoints but a trend for lower stage among those with b2a2 transcripts. No correlation was found either for genomic breakpoint site or BCR/ABL RNA transcript in terms of duration of chronic phase or survival. When stratified by randomized therapy, either interferon-alpha or standard chemotherapy, no difference was noted in relation to genomic breakpoint site or BCR/ABL transcript. Cytogenetic response was not related to the molecular findings.
对219例Ph阳性慢性髓性白血病(CML)患者和15例Ph阴性、BCR阳性CML患者进行了分析,以确定断点位置及其与临床特征、细胞遗传学反应、慢性期持续时间和生存率的关系。对其中119例患者进行了RNA分析,以确定BCR/ABL转录本的类型,并以类似方式进行了分析。诊断时的表现特征,包括年龄、性别、白细胞计数和血小板计数,在具有5'和3'断点的患者与具有b2a2或b3a2 BCR/ABL转录本的患者之间没有显著差异。然而,在一组初诊时白细胞计数<100×10⁹/L的患者亚组中,具有b3a2转录本的患者血小板计数显著更高。根据Sokal风险分组进行分析,5'或3'断点之间没有差异,但具有b2a2转录本的患者分期有降低趋势。在慢性期持续时间或生存率方面,未发现基因组断点位置或BCR/ABL RNA转录本之间存在相关性。当按随机治疗分层,即α干扰素或标准化疗时,在基因组断点位置或BCR/ABL转录本方面未发现差异。细胞遗传学反应与分子学结果无关。