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用表鬼臼毒素VP16 - 213治疗EB病毒诱导的淋巴增殖性疾病。

Treatment of EBV-induced lymphoproliferative disorder with epipodophyllotoxin VP16-213.

作者信息

Migliorati R, Castaldo A, Russo S, Porta F, Fiorillo A, Guida S, Poggi V, Guarino A

机构信息

Department of Paediatrics, University Federico II of Naples, Italy.

出版信息

Acta Paediatr. 1994 Dec;83(12):1322-5. doi: 10.1111/j.1651-2227.1994.tb13030.x.

DOI:10.1111/j.1651-2227.1994.tb13030.x
PMID:7734883
Abstract

A case of haemophagocytic lymphohistiocytosis consistent with X-linked lymphoproliferative disorder is described. Remission was observed after administration of VP-213, a cytotoxic drug generally used to treat histiocytosis. The child is currently in good clinical health.

摘要

描述了一例符合X连锁淋巴增殖性疾病的噬血细胞性淋巴组织细胞增生症病例。给予VP - 213(一种通常用于治疗组织细胞增多症的细胞毒性药物)后观察到病情缓解。该患儿目前临床状况良好。

相似文献

1
Treatment of EBV-induced lymphoproliferative disorder with epipodophyllotoxin VP16-213.用表鬼臼毒素VP16 - 213治疗EB病毒诱导的淋巴增殖性疾病。
Acta Paediatr. 1994 Dec;83(12):1322-5. doi: 10.1111/j.1651-2227.1994.tb13030.x.
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[X-chromosome recessive lymphoproliferative disease (XLP): molecular genetic studies].
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[X-chromosomal recessively inherited lymphoproliferative syndrome. An analysis of EBV-induced immune deficiency].[X染色体隐性遗传的淋巴增殖综合征。对EB病毒诱导的免疫缺陷的分析]
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X-linked lymphoproliferative syndrome. An immunodeficiency disorder with acquired agammaglobulinemia, fatal infectious mononucleosis, or malignant lymphoma.X连锁淋巴增殖综合征。一种伴有获得性无丙种球蛋白血症、致死性传染性单核细胞增多症或恶性淋巴瘤的免疫缺陷疾病。
Arch Pathol Lab Med. 1981 Mar;105(3):119-21.
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[X-linked lymphoproliferative disorder (Duncan's syndrome). 2 possible clinical cases].
Minerva Pediatr. 1987 May 15;39(9):377-83.
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Epstein-Barr virus and the X-linked lymphoproliferative syndrome.爱泼斯坦-巴尔病毒与X连锁淋巴增殖综合征
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X-linked lymphoproliferative disease.
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A boy with fatal infectious mononucleosis suspected as the first Japanese case of X-linked lymphoproliferative syndrome.一名患有致命传染性单核细胞增多症的男孩被怀疑是日本首例X连锁淋巴增生性综合征病例。
Scand J Infect Dis. 1998;30(6):610-2. doi: 10.1080/00365549850161197.
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Epstein-Barr virus-induced diseases in boys with the X-linked lymphoproliferative syndrome (XLP): update on studies of the registry.X连锁淋巴增生综合征(XLP)男孩中的爱泼斯坦-巴尔病毒诱导疾病:登记研究的最新进展
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引用本文的文献

1
Allogeneic bone marrow transplantation for active Epstein-Barr virus-related lymphoproliferative disease and hemophagocytic lymphohistiocytosis in an infant with severe combined immunodeficiency syndrome.对一名患有严重联合免疫缺陷综合征的婴儿进行异基因骨髓移植,用于治疗活动性爱泼斯坦-巴尔病毒相关淋巴增生性疾病和噬血细胞性淋巴组织细胞增生症。
Bone Marrow Transplant. 2002 Mar;29(6):519-21. doi: 10.1038/sj.bmt.1703396.