阵发性夜间血红蛋白尿症和布加综合征。
Paroxysmal nocturnal haemoglobinuria and Budd-Chiari syndrome.
作者信息
Wyatt H A, Mowat A P, Layton M
机构信息
Department of Child Health, King's College Hospital, Denmark Hill, London.
出版信息
Arch Dis Child. 1995 Mar;72(3):241-2. doi: 10.1136/adc.72.3.241.
Abstract
An 11 year old boy developed pancytopenia, haemolysis, and Budd-Chiari syndrome. The venous thrombosis extended to involve other intra-abdominal vessels before paroxysmal nocturnal haemoglobinuria was recognised as the underlying haematological abnormality. Earlier diagnosis would have made curative bone marrow transplantation a possibility.
摘要
一名11岁男孩出现了全血细胞减少、溶血和布加综合征。在阵发性夜间血红蛋白尿被确认为潜在的血液学异常之前，静脉血栓形成已扩展至累及其他腹内血管。早期诊断本可使治愈性骨髓移植成为可能。
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