伴有先天性全身脂肪营养不良的梭菌性气性坏疽：一例报告

Clostridial gas gangrene associated with congenital generalized lipodystrophy: report of a case.

作者信息

Nakae H, Endo S, Yamada Y, Takakuwa T, Taniguchi S, Kikuchi M

机构信息

Critical Care and Emergency Center, Iwate Medical University, Morioka, Japan.

出版信息

Surg Today. 1994;24(12):1097-100. doi: 10.1007/BF01367464.

DOI:10.1007/BF01367464

PMID:7780235

Abstract

Congenital generalized lipodystrophy (CGL) is a rare disease, the main symptoms of which are a reduction of systemic subcutaneous fat, characteristic facial features, hypertrichosis, and insulin-resistant diabetes. We report herein the unusual case of a 25-year-old man with CGL in whom gas gangrene developed, an association which has never before been encountered.

摘要

先天性全身脂肪营养不良（CGL）是一种罕见疾病，其主要症状为全身皮下脂肪减少、特征性面部容貌、多毛症以及胰岛素抵抗性糖尿病。我们在此报告一例罕见病例，一名25岁患有CGL的男性发生了气性坏疽，此前从未有过这种关联的报道。