Fisicaro M, Tonizzo M, Pozzi Mucelli R, Pincetti E, Casagrande S, Carraro N, Bussani R
Department of Internal Medicine, University of Trieste, Italy.
Int Angiol. 1994 Dec;13(4):347-50.
A case of multivessel fibromuscular dysplasia involving the cervico-cephalic arteries, the right renal artery and the iliac arteries is reported. It was associated with reversible bilateral internal carotid arteries and vertebral arteries dissection, left thalamic infarct, right hemorrhagic cerebellar infarct, renovascular hypertension and intermittent claudication of the right lower limb. This report indicates that fibromuscular dysplasia is a systemic angiopathy. Renovascular hypertension may foster the appearance of complication such as dissection of the arteries affected by fibromuscular dysplasia. In the case investigated the dissection of cervico-cephalic arteries was followed by spontaneous healing and a favourable neurological outcome whereas at the iliac arteries a rapid deterioration was observed.
报告了一例多支血管纤维肌发育不良病例，累及颈脑动脉、右肾动脉和髂动脉。它与双侧颈内动脉和椎动脉可逆性夹层、左侧丘脑梗死、右侧出血性小脑梗死、肾血管性高血压和右下肢间歇性跛行有关。本报告表明，纤维肌发育不良是一种系统性血管病。肾血管性高血压可能促使纤维肌发育不良所累及动脉出现夹层等并发症。在所研究的病例中，颈脑动脉夹层后自发愈合且神经功能预后良好，而髂动脉则观察到病情迅速恶化。
