Carter D A, Kim K, Brinker R A
Department of Neurological Surgery, Medical College of Ohio, Toledo 43699, USA.
Surg Neurol. 1995 Mar;43(3):257-60. doi: 10.1016/0090-3019(95)80009-6.
Myelopathy in Klippel-Trenaunay-Weber syndrome is uncommon but has been reported secondary to spinal vascular malformations.
A patient with Klippel-Trenaunay-Weber syndrome who presented with spinal cord compression from a spinal extradural mass lesion (angiomyolipoma) is described.
This association has not been reported previously but is consistent with the segmental vascular abnormalities observed in Klippel-Trenaunay-Weber syndrome.
克-特-韦综合征(Klippel-Trenaunay-Weber syndrome)中的脊髓病并不常见,但已有继发于脊髓血管畸形的相关报道。
本文描述了一名患有克-特-韦综合征的患者,该患者因脊髓硬膜外肿块病变(血管平滑肌脂肪瘤)导致脊髓受压。
此前尚未有这种关联的报道,但这与在克-特-韦综合征中观察到的节段性血管异常是一致的。