Unilateral pseudo-Kaposi's sarcoma (Bluefarb-Stewart type).

Unilateral pseudo-Kaposi's sarcoma has been associated with Klippel-Trenaunay syndrome. A case is described here of a 17-year-old man in whom clinical and histopathologic findings suggested pseudo-Kaposi's sarcoma of this type. In addition to Kaposi's sarcoma, this entity should be differentiated from lymphangioendothelioma and lymphangioma. Positive factor VIII reactivity, which is evident in our case, may eliminate confusion.