Sasaki H, Tozuka K, Hashimoto S, Nagai J, Yazaki T, Tokue A
Department of Urology, Jichi Omiya Medical Center.
Nihon Hinyokika Gakkai Zasshi. 1994 Nov;85(11):1687-90. doi: 10.5980/jpnjurol1989.85.1687.
A 34-year-old woman with tuberous sclerosis presented with an increase of an abdominal mass and intermittent left flank pain on May 20, 1991. Computed tomography showed multiple bilateral renal masses with fatty density areas and a fatty density thrombus in the inferior vena cava, which extended through the right renal vein of the right kidney on ultrasonography. The inferior vena caval thrombus was also demonstrated by magnetic resonance imaging. Since marked deterioration of the right renal function was found on renography, right radical nephrectomy with thrombectomy was performed on July 2. Microscopically all tumors were identical with angiomyolipoma. She was discharged on Jury 20 and had been followed with good renal function at the outpatient clinic for more than 2 years. Follow up CT revealed no interval changes in the left renal masses.
一名34岁的结节性硬化症女性患者于1991年5月20日出现腹部肿块增大及间歇性左胁腹痛。计算机断层扫描显示双侧多个肾脏肿块伴脂肪密度区,下腔静脉有脂肪密度血栓,超声检查显示该血栓延伸至右肾的右肾静脉。磁共振成像也显示了下腔静脉血栓。由于肾图检查发现右肾功能明显恶化,于7月2日进行了右肾根治性切除术及血栓切除术。显微镜下所有肿瘤均与血管平滑肌脂肪瘤一致。她于7月20日出院,在门诊随访超过2年,肾功能良好。随访CT显示左肾肿块无间隔期变化。