van Roekens C N, Zuckerberg A L
Division of Emergency Medicine, Johns Hopkins Hospital, Baltimore, Maryland.
Ann Emerg Med. 1995 Feb;25(2):256-8. doi: 10.1016/s0196-0644(95)70335-7.
We report the case of a 3-month-old girl with tetralogy of Fallot who was resuscitated from a near-fatal hypercyanotic episode (Tet spell). While tetralogy of Fallot is rare (1 in 10,000 live births), failures of diagnosis or management may result in catastrophic outcomes for an eminently survivable condition. An understanding of the pathophysiology of hypercyanotic spells will allow the emergency specialist to understand and apply a treatment option--compression of the abdominal aorta--not previously reported in the emergency medicine literature.
我们报告了一名患有法洛四联症的3个月大女孩的病例，她从一次近乎致命的重度发绀发作（法洛四联症发作）中复苏。虽然法洛四联症很罕见（每10000例活产中有1例），但诊断或治疗失败可能会给这种完全可存活的疾病带来灾难性后果。了解重度发绀发作的病理生理学将使急诊专科医生理解并应用一种治疗方法——腹主动脉压迫，这在急诊医学文献中此前尚未有报道。
