Espinosa Aguilar M D, López de Hierro Ruiz M, Pinel Julián L M, González Galilea A, Suárez Crespo J F, Ruiz-Cabello M, Martín-Vivaldi R
Servicio de Aparato Digestivo, Ciudad Sanitaria Virgen de las Nieves, Granada.
Rev Esp Enferm Dig. 1994 Nov;86(5):849-52.
We present the case of a 56 year old woman with Caroli's disease associated to congenital liver fibrosis, renal nephrocalcinosis and cutaneous vasculitis of the legs. Clinical signs of portal hypertension were treated by a shunt technique. After an asymptomatic period, the patient suffers now from crisis of angiocholitis.
我们报告一例56岁女性患者，患有与先天性肝纤维化、肾钙质沉着症和腿部皮肤血管炎相关的卡罗利病。门静脉高压的临床症状通过分流术进行治疗。在一段无症状期后，患者现在出现了胆管炎发作。
