Boutin C, Davignon A, Fournier A, Houyel L, Van Doesburg N
Service de cardiologie infantile de l'hôpital Sainte-Justine, Montréal, Québec, Canada.
Arch Mal Coeur Vaiss. 1994 May;87(5):663-6.
The authors compared 30 patients with at least one clinical sign of idiopathic dilatation of the pulmonary artery, with a group of 20 normal control subjects in order to establish diagnostic criteria for this condition. In the first group, 17 had characteristic radiological findings and 13 others had clinical signs of idiopathic dilatation of the pulmonary artery. Comparison with the control group showed significant differences (p < 0.05) in 4 parameters: 1) the diameter of the pulmonary artery at the bifurcation/m2 body surface area (2.8 +/- o.4 cm versus 2.4 +/- 0.4 cm), 2) the diameter of the aorta 2 cm beyond the aortic valve/m2 of body surface area (1.7 +/- 0.3 cm versus 2.1 +/- 0.7 cm), 3) the ratio of pulmonary artery/aortic diameters at the valve rings (1.4 +/- 0.2 versus 1.1 +/- 0.02); 4) the ratio of the aorta 2 cm beyond the valve/aortic ring (1.02 +/- 0.07 versus 1.09 +/- 0.09). The diagnostic criteria of idiopathic dilatation of the pulmonary artery in the absence of cardiac or pulmonary disease are: 1) ratio of pulmonary artery diameter at its bifurcation/aortic ring diameter or 2 cm beyond the aortic valve of > or = 1.4; 2) ratio of pulmonary/aortic ring diameters > or = 1.5.
作者将30例至少有一项特发性肺动脉扩张临床体征的患者与20名正常对照者进行比较，以确立该病的诊断标准。在第一组中，17例有特征性影像学表现，另外13例有特发性肺动脉扩张的临床体征。与对照组比较，4项参数存在显著差异（p<0.05）：1）肺动脉分叉处直径/体表面积（2.8±0.4cm对2.4±0.4cm）；2）主动脉瓣上2cm处主动脉直径/体表面积（1.7±0.3cm对2.1±0.7cm）；3）瓣环处肺动脉/主动脉直径比值（1.4±0.2对1.1±0.02）；4）瓣膜上2cm处主动脉/主动脉环比值（1.02±0.07对1.09±0.09）。无心脏或肺部疾病的特发性肺动脉扩张的诊断标准为：1）肺动脉分叉处直径/主动脉环直径或主动脉瓣上2cm处直径比值≥1.4；2）肺动脉/主动脉环直径比值≥1.5。
