Fernbach S K, Zawin J K, Lebowitz R L
Radiology Department, Children's Memorial Hospital, Chicago, IL 60614.
AJR Am J Roentgenol. 1995 Mar;164(3):701-4. doi: 10.2214/ajr.164.3.7863898.
The purpose of our study was to identify the radiographic signs that aid in the diagnosis of obstruction of the ureteropelvic junction of the lower pole (or moiety) of the kidney in children with complete duplication of the ureter and to describe the imaging appearance of this unusual cause of lower-pole hydronephrosis.
We reviewed the medical records and imaging studies of 16 children (11 boys and five girls) with complete ureteral duplication and ureteropelvic junction obstruction of the lower pole of the kidney over a 5-year period. standard criteria for determining urinary tract obstruction were used.
Sonograms showed a lower-pole abnormality (hydronephrosis or cystic mass) in all 15 children who underwent sonography. Voiding cystourethrography, performed for all children, showed vesicoureteral reflux into the lower pole in addition to ureteropelvic junction obstruction in eight children (seven boys and one girl). For the other eight, the diagnosis of lower-pole ureteropelvic junction obstruction was made by excretory urography, at times complemented with diuretic renography or retrograde ureterography.
Ureteropelvic junction obstruction of the lower pole of the kidney in children with complete duplication of the ureter should be a diagnostic consideration when there is dilatation of the lower moiety. Imaging changes parallel those of ureteropelvic junction obstruction in a nonduplicated system. This anomaly, unlike others seen in duplication, appears to be more common in boys than in girls.
我们研究的目的是确定有助于诊断输尿管完全重复畸形患儿下极(或部分)肾盂输尿管连接处梗阻的影像学征象,并描述这种导致下极肾积水的不寻常病因的影像学表现。
我们回顾了16例(11例男孩和5例女孩)在5年期间患有输尿管完全重复畸形且下极肾盂输尿管连接处梗阻的患儿的病历和影像学检查。采用了确定尿路梗阻的标准。
在接受超声检查的所有15例患儿中,超声检查均显示下极异常(肾积水或囊性肿块)。所有患儿均进行了排尿性膀胱尿道造影,除8例(7例男孩和1例女孩)存在肾盂输尿管连接处梗阻外,还显示有膀胱输尿管反流至下极。对于另外8例患儿,下极肾盂输尿管连接处梗阻的诊断是通过排泄性尿路造影做出的,有时辅以利尿肾图或逆行输尿管造影。
当输尿管完全重复畸形患儿下部分出现扩张时,应考虑下极肾盂输尿管连接处梗阻的诊断。影像学改变与非重复系统中的肾盂输尿管连接处梗阻相似。与重复畸形中所见的其他异常不同,这种异常在男孩中似乎比女孩更常见。