Dreyer L, Jacyk W K, du Plessis D J
Department of Anatomical Pathology, University of Pretoria, Republic of South Africa.
Pediatr Dermatol. 1994 Dec;11(4):335-7. doi: 10.1111/j.1525-1470.1994.tb00100.x.
A 13-year-old boy with Peutz-Jeghers syndrome (PJs), gynecomastia, and bilateral multifocal testicular tumors is described. Histology of the testicular tissue disclosed large-cell calcifying Sertoli cell tumors. Females with PJs are known to be at increased risk of developing gonadal tumors. This case and a review of other reported cases suggest that males with PJs are also at risk for developing gonadal tumors.
本文描述了一名患有黑斑息肉综合征(PJs)、男性乳房发育症和双侧多灶性睾丸肿瘤的13岁男孩。睾丸组织的组织学检查显示为大细胞钙化性支持细胞瘤。已知患有PJs的女性发生性腺肿瘤的风险增加。该病例及对其他报道病例的回顾表明,患有PJs的男性也有发生性腺肿瘤的风险。