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多脾伴严重心血管畸形且生存期延长。

Polysplenia accompanied by major cardiovascular anomalies with prolonged survival.

作者信息

Hojo Y, Kuroda T, Yamasawa M, Miyashita H, Seino Y, Mitsuhashi T, Sekiguchi H, Shiina A, Shimada K

机构信息

Department of Cardiology, Jichi Medical School, Tochigi.

出版信息

Intern Med. 1994 Jun;33(6):357-9. doi: 10.2169/internalmedicine.33.357.

Abstract

A 52-year-old female with polysplenia accompanied by major cardiovascular anomalies (a ventricular septal defect, atrial septal defect, persistent left superior vena cava, absent inferior vena cava with a hemiazygos connection and visceral heterotaxia) is reported. She underwent successful surgical treatment and showed prolonged survival.

摘要

报告了一名52岁患有多脾综合征并伴有主要心血管异常(室间隔缺损、房间隔缺损、永存左上腔静脉、下腔静脉缺如伴半奇静脉连接和内脏异位)的女性。她接受了成功的手术治疗,并显示出较长的生存期。

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