Bucsi L, Neumark T, Bossányi A
SOTE Ortopédiai Klinika, Budapest.
Magy Traumatol Ortop Kezseb Plasztikai Seb. 1994;37(3):273-8.
The results of 3 bone biopsies in patients with Sillence I. type of osteogenesis imperfecta are described. The biopsy material was examined with light microscope histomorphometric and various electron microscopic methods. Histomorphometry showed that the osteoid rim (OS%) and the steroid surface covered by osteoblasts (OB%) was significantly greater, in the same time the relative quantity of osteoid (Vvos%) was significantly less, compared with the normal bone. Electron microscopy showed the broadening and unevenness of the mineralization front. The diameters of the collagen fibers were quite unstable compared with the control. The structure of the newly developed apatit crystals was not different, although their measure was less than of the control. The microanalytical examinations of Ca/P relation of the crystal phase did not show any difference.
描述了3例I型成骨不全(Sillence I型)患者的骨活检结果。用光学显微镜组织形态计量学和各种电子显微镜方法对活检材料进行了检查。组织形态计量学显示,与正常骨相比,类骨质边缘(OS%)和成骨细胞覆盖的骨表面(OB%)明显更大,同时类骨质的相对量(Vvos%)明显更少。电子显微镜显示矿化前沿变宽且不均匀。与对照组相比,胶原纤维的直径相当不稳定。新形成的磷灰石晶体的结构没有差异,尽管其尺寸小于对照组。对晶相的Ca/P关系进行的微分析检查未显示任何差异。