Bic J F, Fade-Schneller O, Marie B, Neimann J L, Anthoine D, Martinet Y
Clinique Pneumologique, Hôpital de Brabois, CHU de Nancy, Vandoeuvre-lès-Nancy, France.
Eur Respir J. 1994 Jun;7(6):1194-6.
Cardiac angiosarcoma is a rare tumour with very poor prognosis especially in patients with metastatic disease. We present the case of a 43 year old patient with angiosarcoma revealed by open lung biopsy for multiple pulmonary metastases. Cardiac symptoms were limited to a moderate pericarditis and no echocardiographic sign of heart tumour was observed. The clinical outcome was rapidly fatal despite chemotherapy. The cardiac primary tumour was diagnosed at autopsy. We emphasize the difficulties of diagnosing cardiac angiosarcoma and confirm the limited value of echocardiography for this diagnosis.
心脏血管肉瘤是一种罕见的肿瘤，预后很差，尤其是在患有转移性疾病的患者中。我们报告了一例43岁的血管肉瘤患者，该患者因多处肺转移经开放式肺活检确诊。心脏症状仅限于中度心包炎，未观察到心脏肿瘤的超声心动图征象。尽管进行了化疗，但临床结局很快就致命了。心脏原发性肿瘤在尸检时被诊断出来。我们强调了诊断心脏血管肉瘤的困难，并证实了超声心动图在该诊断中的价值有限。
