Tomlinson R J, Wolfe M W, Nadall J M, Bennett J T, MacEwen G D
Department of Orthopaedic Surgery, Tulane University School of Medicine, New Orleans, Louisiana 70112.
J Pediatr Orthop. 1994 Sep-Oct;14(5):580-5. doi: 10.1097/01241398-199409000-00005.
We attempted to characterize the signs and symptoms of patients presenting with scoliosis as a manifestation of occult syringomyelia, and to determine the effect of syrinx decompression on the deformity and neurologic deficits. This study represented 21 patients treated from 1981 through 1991 at the authors' institution. All patients with occult syringomyelia and no other central nervous system lesions underwent decompression of the syrinx, with improvement in neurologic signs and symptoms. Three of the four with scoliosis that were not treated by arthrodesis showed improvement of their deformity at an average follow-up of 35 months. Three of five patients with myelodysplasia, occult syringomyelia, and scoliosis not previously treated with spinal arthrodesis showed stabilization or improvement of their deformity at an average follow-up of 21 months. We conclude that syringomyelia is associated with a high incidence of developmental scoliosis, and that decompression of the syrinx leads to improvement in, or stabilization of, the majority of scoliotic curves, or postpones the need for fusion.
我们试图描述以隐性脊髓空洞症为表现的脊柱侧凸患者的体征和症状，并确定脊髓空洞减压对畸形和神经功能缺损的影响。本研究纳入了1981年至1991年在作者所在机构接受治疗的21例患者。所有患有隐性脊髓空洞症且无其他中枢神经系统病变的患者均接受了脊髓空洞减压术，神经体征和症状均有改善。4例未接受融合手术治疗的脊柱侧凸患者中，有3例在平均35个月的随访中畸形得到改善。5例脊髓发育不良、隐性脊髓空洞症和脊柱侧凸且此前未接受脊柱融合手术治疗的患者中，有3例在平均21个月的随访中畸形得到稳定或改善。我们得出结论，脊髓空洞症与发育性脊柱侧凸的高发病率相关，脊髓空洞减压可使大多数脊柱侧凸曲线得到改善或稳定，或推迟融合手术的需要。
