Stepanov E A, Krasovskaia T V, Muratov I D, Kobzeva T N, Golodenko N V, Vavilova T I
Khirurgiia (Mosk). 1994 Aug(8):18-21.
The authors examined and treated 52 newborn babies and infants with Hirschsprung's disease. The total form was encountered in 25%, the subtotal in 23.1%, the rectosigmoid in 36.5%, the rectal in 9.6%, and the supraanal in 5.8% of cases. The clinical picture was characterized by retention of meconium (94.2%), regurgitation or vomiting (75%), abdominal distention (100%). Irrigography with calculation of the rectosigmoid ratio was conducted in 35 children, histochemical examination in 46, and histological examination in 38 children. Twenty-four (68.5%) children had the third phase of disturbed proportion of the intestinal bacteria with clinical manifestations of enterocolitis. Emergency decompression of the intestine for low acute intestinal obstruction was carried out in 27 newborn babies. Twenty children were subjected to radical surgery in the first 2-4 months of life. The choice of the operative method was guided by the form of the disease and the length of the aganglionic zone.
作者对52例患有先天性巨结肠症的新生儿和婴儿进行了检查和治疗。全结肠型占25%，次全结肠型占23.1%，直肠乙状结肠型占36.5%，直肠型占9.6%，肛门上型占5.8%。临床表现为胎粪潴留（94.2%）、反流或呕吐（75%）、腹胀（100%）。对35名儿童进行了直肠乙状结肠比率计算的灌肠造影检查，46名儿童进行了组织化学检查，38名儿童进行了组织学检查。24名（68.5%）儿童出现肠道细菌比例失调的第三阶段，并伴有小肠结肠炎的临床表现。27名新生儿因低位急性肠梗阻接受了紧急肠道减压。20名儿童在出生后的前2至4个月接受了根治性手术。手术方法的选择以疾病类型和无神经节区的长度为依据。
