de Chadarévian J P, Lischner H W, Karmazin N, Pawel B R, Schultz T E
Department of Pathology, St. Christopher's Hospital for Children, Philadelphia, Pennsylvania.
Mod Pathol. 1994 Aug;7(6):685-9.
This report describes the case of a 14-yr-old hemophiliac who died of complications of primary pulmonary hypertension. He was infected with the human immunodeficiency virus. The autopsy disclosed that he also had membranoproliferative glomerulonephritis type III and hepatic cirrhosis, both clinically unsuspected. This is the second report describing the association of membranoproliferative glomerulonephritis type III and primary pulmonary hypertension in an HIV-infected patient and the first to consider cirrhosis as a possible additional element of the syndrome.
本报告描述了一名14岁血友病患者死于原发性肺动脉高压并发症的病例。他感染了人类免疫缺陷病毒。尸检发现他还患有III型膜增生性肾小球肾炎和肝硬化，这两种疾病在临床上均未被怀疑。这是第二篇描述HIV感染患者中III型膜增生性肾小球肾炎与原发性肺动脉高压关联的报告，也是第一篇将肝硬化视为该综合征可能的附加因素的报告。
