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[来自血小板血型(HPA)分型供者的血小板输注用于新生儿和胎儿的同种免疫性血小板减少症]

[Platelet transfusion from HPA typed donors in alloimmune thrombocytopenia of newborns and fetuses].

作者信息

Maślanka K, Zupańska B, Debski R, Jakubowska M, Radomska I, Dzieciatkowska A

机构信息

Instytut Hematologii i Transfuzjologii, Warszawa.

出版信息

Acta Haematol Pol. 1994;25(3):215-20.

PMID:7992593
Abstract

The registry of donors typed for HPA-1 and HPA-3 antigens is presented. Three cases of fetal/neonatal alloimmune thrombocytopenia (F/NAIT) transfused with typed platelets either from mother or from registered donors are discussed. All children were transfused just after delivery, one in addition in utero: they survived not having any haemorrhagic complications in central nervous system inspite of such complications in previous born siblings. In the paper the general rules of platelet transfusions in F/NAIT are discussed.

摘要

本文展示了针对血小板特异性抗原1(HPA-1)和血小板特异性抗原3(HPA-3)进行血型分型的供者登记情况。文中讨论了3例胎儿/新生儿同种免疫性血小板减少症(F/NAIT)病例,这些病例输注了来自母亲或登记供者的血型匹配血小板。所有患儿均在出生后立即接受输血,其中1例还在子宫内接受了输血:尽管其之前出生的兄弟姐妹有出血并发症,但这些患儿存活下来,且中枢神经系统未出现任何出血并发症。本文还讨论了F/NAIT中血小板输血的一般规则。

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