Chelli H, Lebbi I, Ayed M, Kchir N
Centre de Maternité et de Néonatologie de la Rabta, Tunis.
J Gynecol Obstet Biol Reprod (Paris). 1994;23(6):681-4.
We report a rare case of uro-genital malformation in 18 years old girl. The malformation associate total septus uteri, hemivagina atretica dextra and homolateral dysplastic kidney. Dysmenorrhea, purulent discharges from cervix and vaginal tumor evocated the diagnosis, which was confirmed by ultrasonography, hysteroscopy and coelioscopy. Therapeutic attitude was total resection of vaginal septus and right nephrectomy. At today, seven cases were published in international literature. In all cases, renal aplasia was reported. Embryologic acknowlegements can't explain this malformation.
我们报告了一例18岁女孩罕见的泌尿生殖系统畸形病例。该畸形伴有完全性子宫纵隔、右侧闭锁半阴道和同侧发育不良肾。痛经、宫颈脓性分泌物和阴道肿物引发了诊断，经超声、宫腔镜和腹腔镜检查得以确诊。治疗方法是完全切除阴道纵隔和右肾切除术。目前，国际文献已发表七例此类病例。所有病例均报告有肾发育不全。胚胎学知识无法解释这种畸形。
