Tange M R, Midholm S, Sindet-Petersen S, Christensen L
Arhus Kommunehospital, neurokirurgisk afdeling.
Ugeskr Laeger. 1994 Mar 7;156(10):1459-65.
The incidence of premature craniosynostosis is 1:2000-1:4000. Ninety percent of these are simple synostosis with premature closure of one or more of the cranial sutures causing reduced or arrested growth perpendicular to the closed suture(s). Ten percent are more complex craniofacial syndromes, where hypoplasia of the maxilla is also of importance to the development of the orbits. The reduced intracranial volume may result in an increased intracranial pressure and is a contributing factor to the rather high frequency of mental retardation seen in patients with premature craniosynostosis. Early correction is necessary in order to achieve a satisfactory cosmetic result as well as prevention of secondary damage to the brain. Craniofacial syndromes with facial hypoplasia require a staged multi-disciplinary treatment. Patients with simple craniosynostosis have to be treated within the first six months after birth.
早发性颅骨缝早闭的发病率为1:2000至1:4000。其中90%为单纯性缝早闭,即一条或多条颅缝过早闭合,导致垂直于闭合缝的生长减缓或停滞。10%为更复杂的颅面综合征,上颌骨发育不全对眼眶发育也很重要。颅内体积减小可能导致颅内压升高,这是早发性颅骨缝早闭患者智力发育迟缓发生率较高的一个促成因素。为了获得满意的美容效果并防止对大脑造成继发性损害,早期矫正很有必要。伴有面部发育不全的颅面综合征需要分阶段进行多学科治疗。单纯性颅骨缝早闭的患者必须在出生后的头六个月内接受治疗。