Van Damme H, Deprez M, de Leval L, Vahdat O, Calteux N, Boniver J, Limet R
Département de Chirurgie Cardio-Vasculaire, CHU du Sart-Tilman, Liège, Belgique.
J Mal Vasc. 1994;19(1):62-5.
The authors observed the spontaneous rupture of a dysplastic superficial femoral artery in a 47 years old patient with Von Recklinghausen disease. The patient presents a gigantism of his right lower limb. On angiography, the femoropopliteal axis is polyaneurysmal and there is evidence of rupture at mid-thigh. The diseased artery is excluded by interposition of a dacron prosthesis, with reimplantation of the deep femoral artery. Histology shows fibrohyalin thickening of the intima. Dysplasia of large limb arteries is excessively rare in Von Recklinghausen disease.
作者观察到一名47岁患有冯·雷克林霍增氏病（神经纤维瘤病）的患者，其发育异常的股浅动脉发生自发性破裂。该患者右下肢呈巨人症。血管造影显示，股腘动脉轴呈多发性动脉瘤，且大腿中部有破裂迹象。通过植入涤纶人工血管并重新植入股深动脉，将病变动脉排除。组织学检查显示内膜纤维透明增厚。在冯·雷克林霍增氏病中，大肢体动脉发育异常极为罕见。
